Bicoronal Synostosis
Bicoronal Synostosis
Bicoronal Synostosis is a rare but serious form of craniosynostosis in which both coronal sutures—located on either side of the skull—fuse prematurely. This early fusion restricts front-to-back skull growth, leading to a shortened head, a tall or tower-like skull shape (turricephaly), and often elevated eye sockets and facial asymmetry. Early diagnosis and expert treatment are essential to support healthy brain development, relieve pressure inside the skull, and restore a more natural head shape.
The coronal sutures run from each ear to the top of the skull. In bicoronal synostosis, both sutures close too early, preventing the skull from expanding front to back. As a result, the head becomes short, wide, and tall, often with a flat forehead, elevated or asymmetrical orbits, and visible facial imbalances. This condition can occur as an isolated anomaly or be part of a syndromic craniosynostosis such as Apert, Crouzon, or Pfeiffer syndromes.
Signs & Symptoms
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Broad, short head with vertical elongation (turribrachycephaly)
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Flat or recessed forehead
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Asymmetry of the face and brow
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Possible signs of increased intracranial pressure (irritability, vomiting, delayed milestones)
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Visible ridges along the coronal sutures
Diagnosis
Bicoronal synostosis is diagnosed through :
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Clinical examination of head shape and facial features
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CT scan with 3D reconstruction to confirm suture fusion
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Genetic testing, especially if syndromic features are present
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Neurological evaluation to assess development and rule out pressure-related complications
Prognosis
With timely surgical intervention and proper follow-up, most children with bicoronal synostosis achieve good developmental outcomes and a significant improvement in head and facial shape. Syndromic cases may require multiple procedures over time, depending on the severity.
Why Choose Us
for Bicoronal Synostosis Care?
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Expert craniofacial and pediatric neurosurgery team
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Integrated genetic and developmental support
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Advanced 3D imaging and surgical planning tools
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Safe, proven surgical outcomes with compassionate care
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Family-focused approach with long-term follow-up
Treatment depends on the Type and Severity
Cranial Vault Reconstruction
Surgery is the primary treatment, typically performed between 6 and 12 months of age. The goals are to :
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Allow proper brain and skull growth
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Relieve intracranial pressure (if present)
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Restore a balanced, natural head and facial shape
The procedure involves reshaping and repositioning the skull bones to expand the cranial space and correct the deformity.
